Tags: Disease.
Schizencephaly (from Greek skhizein meaning to split and enkephalos meaning brain) is a rare birth defect characterized by abnormal continuity of grey matter extending from the ependyma of the cerebral ventricles to the pia mater. Type I schizencephaly has a cord of grey matter tissue either with no fluid cleft or with ventricular or cortical lips closing one end of an abnormal fluid cleft through the hemisphere.