Tags: Disease.
Persistent hyperplastic primary vitreous (PHPV) is a rare congenital developmental anomaly of the eye that resultsfollowing failure of the embryological primary vitreous and hyaloid vasculature to regress. It can be present in three forms: purely anterior (persistent tunica vasculosa lentis and persistent posterior fetal fibrovascular sheath of the lens) purely posterior (falciform retinal septum and ablatio falcicormis congenita) and a combination of both.