Tags: Disease.
Asplenia with cardiovascular anomalies also known as Ivemark syndrome and right atrial isomerism is an example of a heterotaxy syndrome. These uncommon congenital disorders are characterized by defects in the heart spleen and paired organs such as the lungs and kidneys. Another name is asplenia-cardiovascular defect-heterotaxy.Right atrial isomerism is named for its discoverer Swedish pathologist Biörn Ivemark.