Tags: Protein.
Methylmalonate-semialdehyde dehydrogenase [acylating] mitochondrial is an enzyme that in humans is encoded by the ALDH6A1 gene.This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene a mitochondrial methylmalonate semialdehyde dehydrogenase catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA.