Tags: Protein.
Lysosomal alpha-glucosidase (also called α-14-glucosidase) is an enzyme that in humans is encoded by the GAA gene. Errors in this gene cause glycogen storage disease type II (Pompe disease).This gene encodes acid alpha-glucosidase which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing.